Congenital Left Pulmonary Artery Agenesis with the Defect of RML Branch of Right Pulmonary Artery

Park, In Seok; Yoo, Duk Ki; Kim, Woo Joong; Moon, Hwa Sik; Song, Jeong Sup; Ro, Jae Chul; Park, Sung Hak; Byun, Hae Won

doi:1985.32.4.283

Tuberc Respir Dis > Volume 32(4); 1985 > Article

Case report

Tuberculosis and Respiratory Diseases 1985;32(4):283-288.
DOI: https://doi.org/10.4046/trd.1985.32.4.283 Published online December 1, 1985.

Congenital Left Pulmonary Artery Agenesis with the Defect of RML Branch of Right Pulmonary Artery

In Seok Park, Duk Ki Yoo, Woo Joong Kim, Hwa Sik Moon, Jeong Sup Song, Jae Chul Ro, Sung Hak Park, Hae Won Byun

Department of Internal Medicine, Catholic Medical College, Seoul, Korea

우측 폐동맥 중엽분지 결손을 동반한 선천성 좌폐동맥부재증 1예 보고

박인석, 유덕기, 김우중, 문화식, 송정섭, 노재철, 박성학, 변해원

Abstract

Còngenital pulmonary artery agenesis has been known as a disease entity since its first description in 1868 by Fraentzel. Madoff, et al., in their review of the subject in 1952, reported the first successful clinical diagnosis of this condition by angiocardiography. Congenital pulmonary artery agenesis. associated with other congenital cardiovascular anomalies is more frequent than an isolated defect. In Korea congenital pulmonary artery agenesis with PDA was first recognized in 1976 and the isolated defect was first confirmed in 1978. A case of the congenital left pulmonary artery agenesis confirmed by pulmonary arteriography in a young Korean female is presented together with a review of the literatures.