A case of Isolated Congenital Absence of the Right Pulmonary Artery

Kwon, In Soon; Park, Seung Mu; Hue, Sung Ho; Kim, Yoo Young; Han, Yong Chul; Min, Hun Ki

doi:1978.25.2.93

Tuberc Respir Dis > Volume 25(2); 1978 > Article

Case report

Tuberculosis and Respiratory Diseases 1978;25(2):93-98.
DOI: https://doi.org/10.4046/trd.1978.25.2.93 Published online June 1, 1978.

A case of Isolated Congenital Absence of the Right Pulmonary Artery

In Soon Kwon, Seung Mu Park, Sung Ho Hue, Yoo Young Kim, Yong Chul Han, Hun Ki Min

Department of Internal Medicine, College of Medicine, Seoul National University, Seoul, Korea

선천성 우측 폐동맥 폐쇄증 1예 보고

권인순, 박승무, 허성호, 김유영, 한용철, 민헌기

Abstract

In 1868, Franzel reported a case of absence of the right Pulmonary artery, associated with multiple congenital cardiac anomalies as an incidental autopsy findings, and in 1952 Madoff and associates reported the first clinically diagnozed case, of a 14-year-old female and this case was confirmed by angiocardiography. In 1956, Emmanuel and Pattison were to count a total of 46 such cases, most of which had been added because of newly refined angiocardiographic techniques. Previous reviews showed that, in gederal, absence of the right pulmonary artery appeared as an isolaled defect, but absence of the left pulmonary artery was associated with several major abnormalities of the heart and great vessels. A case of isolated congenital absence of the right pulmonary artery, diagnozed clinicaIly by angiocardiography, is presented with review. Possible embryogenesis, radiographic and angiocardiographic appearance of this condition is reviewed.