Pulmonary Lymphangiomatosis.

Cho, Yong Seon; Yoo, Jee Hong; Son, Sang Yong; Cho, Hwoang Lae; Kim, Soo Joong; Han, Min Soo; Kang, Hong Mo

doi:1999.47.4.533

Tuberc Respir Dis > Volume 47(4); 1999 > Article

Case Report

Tuberculosis and Respiratory Diseases 1999;47(4):533-537.
DOI: https://doi.org/10.4046/trd.1999.47.4.533 Published online October 1, 1999.

Pulmonary Lymphangiomatosis.

Yong Seon Cho, Jee Hong Yoo, Sang Yong Son, Hwoang Lae Cho, Soo Joong Kim, Min Soo Han, Hong Mo Kang

Department of Internal Medicine, College of Medicine, Kyung Hee University, Seoul, Korea.

Abstract

Pulmonary lymphangiomatosis is a very rare pulmonary lesion with an aggressive potential that occurs mainly in newborns, infants and young children of both sexes. It is characterized by pulmonary abnormalities of lymphatic system, showing an increased number of complex anastomosing lymphatic channels in the pleura, in the subpleural interlobular septa, and along the bronchovascular lymphatic route and uniformly fatal. We report a case of lymphangiomatosis behaving like lymphangioleiomyomatosis in a 26-year-old woman.

Key Words: Pulmonary lymphangiomatosis, Lymphangioleiomyomatosis, Lymphatic system