A Case Report of Primary Mediastinal Malignant Fibrous Histiocytoma

Oh, Jea Duk; Kim, Hyung Jung; Ahn, Chul Min; Kim, Sung Kyu; Lee, Won Young; Jeong, Hyeon Joo; Lee, Kwang Kyl; Lee, Doo Yun

doi:1989.36.4.395

Tuberc Respir Dis > Volume 36(4); 1989 > Article

Case report

Tuberculosis and Respiratory Diseases 1989;36(4):395-400.
DOI: https://doi.org/10.4046/trd.1989.36.4.395 Published online December 1, 1989.

A Case Report of Primary Mediastinal Malignant Fibrous Histiocytoma

Jea Duk Oh¹, Hyung Jung Kim¹, Chul Min Ahn¹, Sung Kyu Kim¹, Won Young Lee¹, Hyeon Joo Jeong², Kwang Kyl Lee², Doo Yun Lee³

¹Department of Internal Medicine, College of Medicine, Yonsei University, Seoul, Korea
²Department of Pathology, College of Medicine, Yonsei University, Seoul, Korea
³Department of Chest surgery, College of Medicine, Yonsei University, Seoul, Korea

종격동에 발생한 악성 섬유성 조직구종 1예

오제덕¹, 김형중¹, 안철민¹, 김성규¹, 이원영¹, 정현주², 이광길², 이두연³

Abstract

The malignant fibrous histiocytoma was first described in 1964 by 0 ’8rien and Stout. Since then, malignant fibrous histiocytoma was recognized as the most common soft tissue sarcoma in adult. lt involves the extremities, retroperitoneum, and trunk. The prognosis is poor and the depth and histologic grade affect survival. The primary mediastinal malignant fibrous histiocytoma is a rare disease of all malignant fibrous histiocytoma We have experienced a case of primary mediastinal malignant fibrous histiocytoma, which was confirmed by biopsy with thoracotomy. Histologically. the tumor in our case was pleomorphic type and the patient received post-operative radiation therapy. We presented a case of primary mediastinal malignant fibrous histiocytoma with review of literatures.