A Case of Pulmonary and Retroperitoneal Lymphangioleiomyomatosis.

Kwak, Nam Ju; Park, Nam Gu; Kim, He Young; Eom, Je Ho; Choi, Meong Chan; Yun, Se Jin; Kim, Sung Taek; Do Lee, Sang

doi:1995.42.4.600

Tuberc Respir Dis > Volume 42(4); 1995 > Article

Case Report

Tuberculosis and Respiratory Diseases 1995;42(4):600-604.
DOI: https://doi.org/10.4046/trd.1995.42.4.600 Published online August 1, 1995.

A Case of Pulmonary and Retroperitoneal Lymphangioleiomyomatosis.

Nam Ju Kwak, Nam Gu Park, He Young Kim, Je Ho Eom, Meong Chan Choi, Se Jin Yun, Sung Taek Kim, Sang Do Lee

Department of Interal Medicine, Chung Buk National University College of Medicine, Cheong Ju, Korea.

Abstract

Lymphangioleiomyomatosis, a rare disease in women of childbearing age, is the result of benign nodular hypertrophy of the smooth muscle of the lypmhatics and other tissues of the abdomen and thorax. We report a 36-years-old woman with pulmonary and retroperitoneal lymphangioleiomyomatosis who responded with hormone treatment. She developed vaginal pruritis and a pelvic ultraound was done given her significant past medical history. Ultrasound examination demonstrated a large mass in the right side of her pelvis. Therefore she was admitted to St. Michael's Hospital in Toronto for laparoscopy. Result of cytology was to be consistent with the diagnosis of retroperitoneal lymphangioleiomyomatosis. High resolution CT sacn of the thorax demonstrated multiple small cystic lesions, without associated nodularity compatible with a diagnosis of pulmonary lymphangioleiomyomatosis. She has been taking Provera tablets l00mg po tid since Dec. 15, 1993. We have given her a prescription for Depo provera 500mg IM monthly since she came back to Korea, and made arrangements for regular follow up monthly. We performed chest X-ray, CT of chest(high resolution), abdomen and pelvis, pulmonary function tests and arterial blood gas analysis. Chest X-ray and CT findings showed no significant change since July. 20, 1993.

Key Words: Pulmonary, Retroperitoneal Lymphangioleiomyomatosis