A Case of Isolated Right Pulmonary Artery Agenesis.

Kim, Do Youn; Lee, Jae Sung; Kim, Young; Chang, Yoon Soo; Kim, Hyung Jung; Kim, Tae Hoon; Ahn, Chul Min

doi:2004.57.5.489

Tuberc Respir Dis > Volume 57(5); 2004 > Article

Case Report

Tuberculosis and Respiratory Diseases 2004;57(5):489-493.
DOI: https://doi.org/10.4046/trd.2004.57.5.489 Published online November 1, 2004.

A Case of Isolated Right Pulmonary Artery Agenesis.

Do Youn Kim, Jae Sung Lee, Young Kim, Yoon Soo Chang, Hyung Jung Kim, Tae Hoon Kim, Chul Min Ahn

¹Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea. Ahnswine@naver.com
²The institute of Chest Disease, Yonsei University College of Medicine, Seoul, Korea.
³Department of Radiology, Yonsei University College of Medicine, Seoul, Korea.

Abstract

Unilateral pulmonary artery agenesis is a rare congenital anomaly usually associated with other cardiovascular anomalies such as tetralogy of Fallot or septal defect. Unilateral pulmonary artery agenesis without other coexisting cardiovascular abnormality (isolated unilateral pulmonary artery) is extremely rare and often asymptomatic until adulthood. In these patients, diagnostic clue is found in a plain chest roentgenogram, showing a hyperlucent contracted hemithorax. We have recently experienced a case of isolated right pulmonary artery agenesis, which was diagnosed by chest dynamic CT, perfusion scan, echocardiogram and 3-dimensional reconstruction cardiac CT angiography in a 50-year old female who had suffered from mild dyspnea on exertion and improved with conservative treatment. We report this case with a brief review of the relevant literature.

Key Words: Isolated right Pulmonary artery agenesis