Pulmonary Lymphangioleiomyomatosis with Chylous Pleural Effusion.

Park, Byung Joon; Cho, Jae Hwa; Moon, Tae Hoon; Park, Sang Joon; Ryu, Jung Seon; Lee, Hong Lyeol; Kwak, Seung Min; Cho, Chul Ho

doi:2001.50.1.127

Tuberc Respir Dis > Volume 50(1); 2001 > Article

Case Report

Tuberculosis and Respiratory Diseases 2001;50(1):127-131.
DOI: https://doi.org/10.4046/trd.2001.50.1.127 Published online January 1, 2001.

Pulmonary Lymphangioleiomyomatosis with Chylous Pleural Effusion.

Byung Joon Park, Jae Hwa Cho, Tae Hoon Moon, Sang Joon Park, Jung Seon Ryu, Hong Lyeol Lee, Seung Min Kwak, Chul Ho Cho

Abstract

Pulmonary lymphangioleiomyomatosis is a disease involving the proliferation of atypical smooth muscle cells trom the perilymphatics, peribronchial and perivascular region of the lung and the retroperitneum. The disease usually affects women of child-bearing age. We recently experienced a case of pulmonary lymphangioleiomyomatosis in a 31-year-old women who had suffered from a chylous pleural effusion. Histologic confirmation of lymphangioleiomyomatosis was made upon a video-associated thoracoscopic lung biopsy. Here we report this case with a brief review of the literature.

Key Words: Lymphangioleiomyomatosis, Chylous pleural effusion