A Case of Systemic Sclerosis Sine Scleroderma Presenting as Pulmonary Interstitial Fibrosis.

Kwak, Jin Ho; Choi, Won Il; Lee, Seung Hyun; Seo, Chang Gyun; Kim, Kyung Chan; Kim, Min Su; Kwon, Kun Young; Suh, Soo Ji; Park, Chang Kwon; Jeon, Young June

doi:2001.50.4.493

Tuberc Respir Dis > Volume 50(4); 2001 > Article

Case Report

Tuberculosis and Respiratory Diseases 2001;50(4):493-498.
DOI: https://doi.org/10.4046/trd.2001.50.4.493 Published online April 1, 2001.

A Case of Systemic Sclerosis Sine Scleroderma Presenting as Pulmonary Interstitial Fibrosis.

Jin Ho Kwak, Won Il Choi, Seung Hyun Lee, Chang Gyun Seo, Kyung Chan Kim, Min Su Kim, Kun Young Kwon, Soo Ji Suh, Chang Kwon Park, Young June Jeon

Abstract

Lung involvement in systemic sclerosis(SSC) is common but usually occurs late in the course. Skin changes usually occur before the pulmonary findings. In this report, a patient who developed pulmonary interstitial fibrosis without skin changes is presented. A diagnosis of SSC lung involvement was made histologically. The a nti-scl-70 antibody test was positive. Esophageal manometry revealed a lower amplitude in the lower two-third of the esophagus and pressure in the lower esophageal sphincter. Here we report a case of wystemic sclerosis sine scleroderma presenting as pulmonary interstitial fibrosis with a review of the relevant literatures.

Key Words: Systemic sclerosis sine scleroderma, Pulmonary interstitial fibrosis