A Case of Primary Pulmonary Hypertension in Pregnancy Presented as Massive Hemoptysis.

Kim, Myung Sook; Kim, Hyoung Doo; Kim, Seok Chan; Kwan, Soon Suk; Kim, Young Kyoon; Kim, Kwan Hyoung; Moon, Hwa Sik; Song, Jeong Sup; Park, Sung Hak

doi:2004.57.1.66

Tuberc Respir Dis > Volume 57(1); 2004 > Article

Case Report

Tuberculosis and Respiratory Diseases 2004;57(1):66-71.
DOI: https://doi.org/10.4046/trd.2004.57.1.66 Published online July 1, 2004.

A Case of Primary Pulmonary Hypertension in Pregnancy Presented as Massive Hemoptysis.

Myung Sook Kim, Hyoung Doo Kim, Seok Chan Kim, Soon Suk Kwan, Young Kyoon Kim, Kwan Hyoung Kim, Hwa Sik Moon, Jeong Sup Song, Sung Hak Park

Department of Internal Medicine, Daejon St. Mary's Hospital, The Catholic University of Korea. cmcksc@catholic.ac.kr

Abstract

Primary pulmonary hypertension (PPH) is a rare, progressive and incurable disease, which is characterized by an increase in the pulmonary artery pressure without a demonstrable cause. The most common presenting symptom is dyspnea on exertion, with other symptoms comprising of chest pain, syncope and hemoptysis. The diagnosis is one of exclusion of any of the known causes of pulmonary hypertension. When associated with pregnancy, the maternal mortality ranges from 30 to 50%. Because pregnancy and labor are very serious problems for patients with PPH, the available evidence suggests that pregnancy when afflicted with PPH should be avoided. In account the case of a 33-year old patient, reporting with massive hemoptysis, and diagnosed with PPH during her twenty seventh week of gestation, is presented. She was treated with conservative management, including oxygen and a vasodilator, and underwent a pregnancy termination. However, due to aggravation of right heart failure, she presented with severe systemic hypotension and hypoxemia, and eventually died. This case is reported, with brief review of the literature.

Key Words: Primary pulmonary hypertension, Pregnancy, Hemoptysis